N | % | |
---|---|---|
Genotyping (PRNP-Codon 129) | ||
Study consented | 25 | 83% |
Of whom tested | 25 | 100% |
MM | 8 | 32% |
MV | 13 | 52% |
VV | 4 | 16% |
Duration of illness (from the onset of symptoms to censor date/death) | ||
MM | Mean = 8.3 years (1.1 – 16.6 years, std dev 5.5) | |
MV | Mean = 10.4 years (4.1 – 17.4 years, std dev 4.6) | |
VV | Mean = 11.3 years (6.6 – 16.6 years, std dev 4.7) | |
Age at onset of symptoms | ||
MM | Mean = 64 years (56 – 79 years, std dev 7.4) | |
MV | Mean = 65 years (53 – 78 years, std dev 7.8) | |
VV | Mean = 63 years (56 – 69 years, std dev 5.4) | |
Gender | ||
MM | Male = 5 (63%), Female = 3 (37%) | |
MV | Male = 8 (62%), Female = 5 (38%) | |
VV | Male = 2 (50%), Female = 2 (50%) | |
Not known | Male = 4 (80%), Female = 1 (20%) |